HPS1 Primary Antibody
Item Information
Catalog #
Size
Price
Description
Hermansky-Pudlak syndrome 1. This protein may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is a component of three different protein complexes termed biogenesis of lysosome-related organelles complex (BLOC)-3, BLOC4, and BLOC5. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 1. Multiple transcript variants encoding distinct isoforms have been identified for this gene; the full-length sequences of some of these have not been determined yet.
Product Overview
Entrez GenelD
3257
Aliases
HPS; MGC5277; HPS1
Clone#
5G12G2
Host / Isotype
Mouse / IgG2a
Species Reactivity
Human
Immunogen
Purified recombinant fragment of HPS1 expressed in E. Coli.
Formulation
Ascitic fluid containing 0.03% sodium azide.
Storage
4°C; -20°C for long term storage
Product Applications
WB (Western Blot)
1/500 - 1/2000
ELISA
1/10000
References
1. Platelets. 2007 Mar;18(2):150-7.
2. Intern Med. 2005 Jun;44(6):616-21.
3. Proc Natl Acad Sci U S A. 2003 Jul 22;100(15):8770-5. Epub 2003 Jul 7.
2. Intern Med. 2005 Jun;44(6):616-21.
3. Proc Natl Acad Sci U S A. 2003 Jul 22;100(15):8770-5. Epub 2003 Jul 7.
Product Image
Western Blot
Figure 1: Western blot analysis using HPS1 mouse mAb against truncated HPS1 recombinant protein (1) and HPS1-hIgGFc transfected CHO-K1 cell lysate (2).
For Research Use Only. Not for use in diagnostic procedures.